Table 4.4-1. Summary of other types of pemphigus

Pemphigus foliaceus (Figure)

– No mucosal involvement

– Usually milder skin lesions on the chest, back, face, and scalp

Pemphigus herpetiformis

– Characterized by grouped, pruritic, vesiculobullous lesions in herpetiform and annular arrangement

– Mucosal involvement is uncommon

Pemphigus vegetans (Figure)

– Characterized by hyperkeratotic, verrucous, vegetative plaques, mostly affecting intertriginous areas

– Involvement of oral mucosa is common

IgA pemphigus (subcorneal pustular dermatosis and intraepidermal neutrophilic IgA dermatosis)

Groups of vesicles and pustules on the erythematous background, mostly on the trunk, proximal extremities, and in intertriginous areas

Paraneoplastic pemphigus

– Severe, painful, hemorrhagic oral erosions and ulcerations extending to lips

– Polymorphic skin lesions (eg, flaccid pemphigus-like blisters; tense pemphigoid-like bullae; erythema multiforme–like, graft-versus-host disease–like, and purple, lichen planus–like lesions)

– Severe bronchiolitis (bronchiolitis obliterans) can also develop