Large-vessel vasculitis |
Takayasu arteritis Giant cell arteritis |
Medium-vessel vasculitis |
Polyarteritis nodosa Kawasaki disease |
Small-vessel vasculitis |
ANCA-associated vasculitis: – Microscopic polyangiitis – Granulomatosis with polyangiitis (Wegener granulomatosis) – Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome) Immune-complex small-vessel vasculitis: – Anti–glomerular basement membrane (anti-GBM) disease – Cryoglobulinemic vasculitis – IgA vasculitis (Henoch-Schönlein purpura) – Hypocomplementemic urticarial vasculitis (anti-C1q vasculitis) |
Variable-vessel vasculitis |
Behçet disease Cogan syndrome |
Single-organ vasculitis |
Cutaneous leukocytoclastic angiitis Cutaneous arteritis Primary central nervous system vasculitis Isolated aortitis Other |
Vasculitis associated with systemic disease |
Lupus vasculitis Rheumatoid vasculitis Sarcoid vasculitis Other |
Vasculitis associated with probable etiology |
Hepatitis C virus–associated cryoglobulinemic vasculitis Hepatitis B virus–associated vasculitis Syphilis-associated aortitis Drug-associated immune-complex vasculitis Drug-associated ANCA-associated vasculitis Cancer-associated vasculitis Other |
Source: Arthritis Rheum. 2013;65(1):1-11. | |
ANCA, antineutrophil cytoplasmic antibody. |